19. X linked sideroblastic anemia is most common form of congenital sideroblastic anemia. The anemia in this disorder responds to :-
1. High dose pyridoxine
2. Low dose pyridoxine
3. High dose hydroxyurea
4. Low dose hydroxyurea
Answer = High dose pyridoxine
In more than half of the patients with XLSA, the anemia responds to high doses of pyridoxine. An initial dose of pyridoxine may be 50–100 mg, albeit higher doses have been reported and lower maintenance doses for responsive individuals may be effective.
